T

HE PIERRE ROBIN syndrome13

is charactenized

by three defects : micrognathia,

cleft palate and glossoptosis. It is a
distinct clinical entity possessing a history
that is almost monotonous in regularity,
and with physical findings so striking as to
not easily be overlooked. Definitive forms
of therapy are available and with proper
management a good prognosis can be given
in the majority of cases. The syndrome is
well documented in the French litenature
but has gained little recognition in the
United States. After encountering a 2month-old white male with Pierre Robin
syndrome and severe bilateral congenital
glaucoma, our attention was directed to
ocular involvement in these cases. Four
such patients with bilateral ocular disease
were subsequently reported.