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R.MANISH PANY
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tIo!ogy
ukuovu
leuiu, commou iu euerai jojuiatiou, vitu
raciai ciusteriu iu liacks
!InIcu! PvesentutIon
Smmetric, asmjtomatic.
luccai mucosa iuoied b ravuite,
di||use, miik sur|ace vitu au ojaiesceut
(uaiit.
Vriukied sur|ace |eatures at rest.
lissijatiou o| cuaues vitu stretcuiu o|
mucosa.
IugnosIs
Ciiuicai recouitiou is su||icieut.
liojs |iudius viii suov marked iutraceiiuiar edema o|
sjiuous iaer.
Iudiiduai ceiis vitu ciear ctojiasm aud comjact uuciei.
`ormai basai ceii iaer.
IIIeventIu! IugnosIs
Cueek cueviu
Iereditar beuiu iutraejitueiiai dskeratosis
Vuite sjoue ueus
licueu jiauus
Caudidiasis
%veutment
`oue uecessar, uo reiatiou to dsjiasia
carciuoma
Keassurauce
PvognosIs
lxceiieut
VII1l SlO`Cl `lVS
tIo!ogy
Iereditar ,autosomaidomiuaut) disorder
o| keratiuizatiou a||ectiu uoukeratiuiziu
orai, esojuaeai, aud auoeuitai mucosai
ejitueiium.
loiut mutatious iu tue keratiu = audor !
eues
tlinicul Prcscntution
.smjtomatic
leeji |oided, tuickeued, vuite mucosa
luccai mucosa cuie|i a||ected
`o |uuctiouai imjairmeut
Iucreased jromiueuce duriu secoud decade
icroscoic Iinoings
larakeratosis, acautuosis, iutraceiiuiar edema
leriuuciear coudeusatiou o| keratiu
iugnosis
Ciiuicai ajjearauce
lamii uistor
Microscojic |iudius
illcrcntiul iugnosis
Idiojatuic ieukojiakia
Cuemicaituermai buru
Curouic iovrade trauma ,morsicatio)
%rcutmcnt
`oue re(uired
`o maiiuaut joteutiai
Prognosis
lxceiieut
IlKllI1.KY ll`IC`
I`1K.llI1IllI.l lYSKlK.1OSIS
944
It is a rare, autosomai domiuaut uereditar
couditiou.
.iso kuovu as Vitkojs disease.
tlinicul Prcscntution
lari ouset o| buibar cou}uuctiitis aud orai vuite iesious.
lrecediu tue buibar cou}uuctiitis are |oam eiatiuous jia(ues tuat
rejreseut tue ocuiar couuterjart o| tue orai mucosai iesious.
Orai iesious cousist o| so|t, asmjtomatic, vuite |oids aud jia(ues o|
sjou mucosa.
.reas cuaracteristicaii iuoied iuciude tue buccai aud iabiai mucosa
aud iabiai commissures, as veii as tue |ioor o| tue moutu aud iaterai
sur|aces o| tue touue, iuia, aud jaiate. 1ue dorsum o| tue touue
is usuaii sjared.
latieuts ma comjiaiu o| juotojuobia, esjeciaii iu eari ii|e.
liiuduess, secoudar to corueai ascuiarizatiou, uas beeu rejorted.
iugnosis
Ciiuicai ajjearauce
lamii uistor
Microscojic |iudius
illcrcntiul iugnosis
Idiojatuic ieukojiakia
Cuemicaituermai buru
Curouic iovrade trauma ,morsicatio)
licueu jiauus
lubus ertuematosus
%rcutmcnt
`oue re(uired
lor eaiuatiou aud treatmeut o| tue ocuiar
iesious, tue jatieut suouid be re|erred to au
ojutuaimoioist.
Prognosis
lxceiieut

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