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    Hemachromatosis is a genetic disease characterized by increased intestinal iron absorption and tissue iron deposition, causing iron to accumulate in the liver and lead to enlargement and cirrhosis. Common clinical manifestations include fatigue, dyspnea, palpitations, and skin discoloration. The goal of nursing care is to remove excess iron through regular phlebotomy of 500mL of blood each week for 2-3 years until iron stores are depleted, then less frequently. Early diagnosis can result in a normal life expectancy.

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    Hemachromatosis is a genetic disease characterized by increased intestinal iron absorption and tissue iron deposition, causing iron to accumulate in the liver and lead to enlargement and cirrhosis. Common clinical manifestations include fatigue, dyspnea, palpitations, and skin discoloration. The goal of nursing care is to remove excess iron through regular phlebotomy of 500mL of blood each week for 2-3 years until iron stores are depleted, then less frequently. Early diagnosis can result in a normal life expectancy.

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    6 views2 pages

    Anemias 9

    Uploaded by

    Tanya
    Hemachromatosis is a genetic disease characterized by increased intestinal iron absorption and tissue iron deposition, causing iron to accumulate in the liver and lead to enlargement and cirrhosis. Common clinical manifestations include fatigue, dyspnea, palpitations, and skin discoloration. The goal of nursing care is to remove excess iron through regular phlebotomy of 500mL of blood each week for 2-3 years until iron stores are depleted, then less frequently. Early diagnosis can result in a normal life expectancy.

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    of 2

    Hemachromatosis

    Genetic disease characterized by


    -increased intestinal iron absorption
    -and increased tissue iron
    deposition
    Secondary iron accumulates in the
    -liver causing enlargement and
    -cirrhosis
    CLINICAL MANIFESTATIONS
    1. Dyspnea on exertion
    2. Fatigue

    NURSING CARE
    How do we fix it?
    THE FIX: Phlebotomy
    THE BAND-AID:

    GOAL remove Excess Iron


    1. Phlebotomy remove 500mL of blood
    - each week for 2-3 years. Until iron
    stores are depleted, then less frequent

    3. Palpitations
    4. Angina
    5. Tachycardia
    6. CHF
    7. MI
    8. Pallor
    9. Puritis
    10. Jaundice
    11. Increased Capillary Refill Time
    12. Bronzing of the skin
    13. Cardiomyopathy
    14. Arthritis
    15. Testicular Atrophy

    Common causes of Death are:


    1. Cirrhosis
    2. Liver Failure
    3. Hepatic Carcinoma
    4. Cardiac Failure

    ***Early Diagnosis life expectancy is


    Normal.

    LABS
    Elevated Iron (Normal 2-6g)
    Elevated Serum Ferritin
    TIBC
    Dx made by Biopsy or Molecular
    Testing.

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