Ebstein’s anomaly is a rare congenital heart disorder occurring in ≈1 per 200 000 live births and

accounting for <1% of all cases of congenital heart disease.2–6 This anomaly was described by
Wilhelm Ebstein in 1866 in a report titled, “Concerning a very rare case of insufficiency of the
tricuspid valve caused by a congenital malformation.”7,8 The patient was a 19-year-old cyanotic
man with dyspnea, palpitations, jugular venous distension, and cardiomegaly.7,8 At autopsy,
Ebstein described an enlarged and fenestrated anterior leaflet of the tricuspid valve. The
posterior and septal leaflets were hypoplastic, thickened, and adherent to the right ventricle.
There was also a thinned and dilated atrialized portion of the right ventricle, an enlarged right
atrium, and a patent foramen ovale9 (Figure 1). By 1950, only 3 cases of this anomaly had been
published