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Eagle Syndrome An Unusual Cause of Head and Neck Pain
Eagle Syndrome An Unusual Cause of Head and Neck Pain
Eagle Syndrome An Unusual Cause of Head and Neck Pain
Eagle Syndrome
An Unusual Cause of Head and Neck Pain
E
AGLE SYNDROME IS COMMENT Though already known to oto-
characterized by re- laryngologists, we hope to increase
current pain in the Eagle syndrome comprises clinical awareness of Eagle syndrome among
oropharynx and face symptoms arising from an elon- neurologists because it is a treat-
due to an elongated gated styloid process or calcified able entity different from glossopha-
styloid process or calcified stylohy- stylohyoid ligament. Otolaryn- ryngeal neuralgia.
oid ligament.1 It must be differenti- gologist W. W. Eagle described
ated from glossopharyngeal neural- the syndrome in 1937 based on Christina K. Sun, MD
gia. We aim to bring Eagle syndrome review of previous communica- Vince Mercuri, MMed, FRANCZR
to the attention of neurologists be- tions and personal cases. 2 Com- Mark J. Cook, MD, FRACP
cause it is underrepresented in neu- plaints include throat pain, for-
rological literature. We present a case eign body sensation, dysphagia,
of a man with left mastoid pain; com- and facial pain,1 often radiating to Correspondence: Dr Sun, Depart-
puted tomographic scan revealed ex- the mastoid or ear.3 Syncope has ment of Neurology, Centre for Clini-
tensive stylohyoid ligament ossifi- also been reported.3 Diagnosis is cal Neurosciences and Neurologi-
cation bilaterally. With appropriate based on history, clinical exami- cal Research, St Vincent’s Hospital
clinical history and radiography, nation, and radiography. Palpa- Melbourne, PO Box 2900, Fitzroy
Eagle syndrome can usually be iden- tion of the styloid process in the VIC 3065, Australia (christinaksun
tified and treated. tonsillar fossa indicates elongation @yahoo.com).
because normal processes are not Author Contributions: Study con-
palpable.1 Panoramic radiography cept and design: Sun and Cook. Ac-
REPORT OF A CASE
of the mouth or computed tomog- quisition of data: Mercuri. Analysis
raphy of the skull base and neck and interpretation of data: Sun and
A 25-year-old man was seen with 3 are the preferred radiographic Mercuri. Drafting of the manuscript:
years of left mastoid pain radiating studies. 4 Medical management Sun. Critical revision of the manu-
to the ear. The pain was constant and includes analgesics, anticonvul- script for important intellectual con-
aching; it peaked over minutes and sants, antidepressants, and local tent: Mercuri and Cook. Administra-
lasted days. Mouth opening, sneez- infiltration with steroids or anes- tive, technical, and material support:
ing, and head turning precipitated thetic agents. 4 Patients who fail Sun, Mercuri, and Cook.
episodes. Head turning occasion- medical therapy may benefit from
ally triggered presyncope. Neuro- surgical removal of the elongated REFERENCES
logical examination and brain mag- portion of the styloid process.1
netic resonance imaging were The pathophysiological mecha- 1. Murtagh RD, Caracciolo JT, Fernandez G. CT find-
unremarkable. Diagnosis was sus- nisms contributing to Eagle syn- ings associated with eagle syndrome. AJNR Am J
pected based on clinical history. drome remain controversial and Neuroradiol. 2001;22:1401-1402.
2. Eagle WW. Elongated styloid processes: report of
Head computed tomography re- include glossopharyngeal nerve two cases. Arch Otolaryngol. 1937;25:584-587.
vealed extensive stylohyoid liga- compression, pharyngeal mucosa 3. Bruyn GW. Stylohyoid syndrome (Eagle). In: Vinken
ment ossification bilaterally irritation by posttonsillectomy PJ, Bruyn GW, Klawans HL, Rose FC, eds. Hand-
(Figure). Over-the-counter pain scarring, and callus formation book of Clinical Neurology. Vol 4. Amsterdam, the
medications and valproate sodium from prior styloid fracture. 1 Netherlands: Elsevier Science Publishers BV; 1986:
501-514.
were ineffective, though local hot- Carotid vessel impingement and 4. Slavin KV. Eagle syndrome: entrapment of the glos-
pack application provided improve- irritation of sympathetic nerves sopharyngeal nerve? case report and review of the
ment. The patient refused surgery. have also been proposed.3 literature. J Neurosurg. 2002;97:216-218.
Figure. Reformatted coronal maximum intensity projection image (A) and volume-rendered reconstruction in bone window (B) of the upper neck data set,
demonstrating near-complete stylohyoid ligament (arrows) ossification, extending from the styloid process tip to the lesser cornu of the hyoid bone bilaterally.