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Cardiomiopatiile
Cardiomiopatiile
CARDIOMIOPATIILE
D. Zdrenghea,D. Rddulesca
dilalotivi.
f,&?.L/. Cardionriofrrle p&aslcrrali
Sccliune axlung .ri&242 ( \4D Secliunc pdrasLdnalid hLnshco_MvM jossittd(i
EcoM DTDvs.rescut nrlenLriculor tcndinli,deegaliarca mltcirii V)l-^ ti V \'l ll Dimcn_
siunilcSlv ti I'l'sunt rcdusciar tapoful DTDVS/SIV,PPcrcscul
u lutg. f.co-M.SAMscvu
(:]r''lllt Scqiuncprrn($nrlndx lung.!co-M lrcizu.r ri&2dA CMHO.Sccliurel)urutleLlxrll
fit!,24,6.
- scpl ll a VM.^.
rlpozilic
pevrlvo6onicll'ousp!!orondi0nn
tr1czosistolici drcaPtI(slgeau).
aspcclde (1ig.24.7).Dis-
SAM (,.sirtolicintefiormo\rclncnt") i f l )P Jri rnrrr In.Jl Jr Jr i r' r drc)r i c> rr(:rV \ (' r,rFrr ', r r t
|anlasistolicnVMA-SIV reprezinin ii ur indjccdc evaluare cu I)P(sauDC) h rcrti. sc stabilcftcnivelulobst colulLriinlre
a scvcridliiobslruclici.cafcesremaximi in cazulapozitiei calc.rdcinlrare $i caleadcicrirc 0 VS ii abscnlagrddicnrulxi
scpralca VMA (fi9.24.8). intre calcadc ic$irea VS ir Ao rsccndentn.
Clrci|ereadimensiunikrrAS (h M $i U)poalcll sccundarl Od.rlatslabilit tivelul obstacolului.ir IX sau DP, drn
adl crctleriiPTI)VS(dislunclirdiastolicaia VS). cerii lM pozilie apicah sau poTilie suprastcnali se poatc cvidcnlia
imaginc.rcurgcrii in caleade iciirc I VS (velocitatcnr..iaLa-
[xaminareaeco-l)opplcroiern date escnlirlc pcnlru gaf')iisepo.rtc slabili gradienlullransslenotic. atit nr rcp&s
cMHO [81.
diagnosricul cat ii in cazul unor nanopere dinamicc (tig.2'1.9)
In Dopplercolorseevidcnliazao imaginede rip mozaic i nt)11& -i | JJU .cbrI D ( n..r,l adrrosri cr< ,/rl )i* r\ a
(curycrcLurbulenti)in calcadc ictire a VS. sub valvclc hreaz6prezenla $i sc!eritateainsuficicnlci iirale secundarc
uacl i oni fi i V MA (Ii g.24.10).
323
In I)(. ri indeosebiin DP sc po{tc evidenlia ii evalxa
dislirnclid diastolicaa VS. dc rcguln. dc 1 p relaxarealterat:
(\.czi rcrformanta vS) L9l.
[co 1)oppleresteinrportrnln ii in elahrarearezxltatc]or
1r3t!mcntuluicll doguri- irlcncDlional sauchinrrgicrl inclu-
si! a unor inten'enliisofisticalccum arfi pacrrg-ul\cnlriculrr
drcpt sau al alcooltani coronrriane.in ioate acene siluarii
nnmaiecogmtiaDopplcr(fi dcsi!ur explorareahclnodimmi
cl invazivi. careestcinsl grcuaccesibili$i aproapeilnposibil
dc cfectuatseda(pc pcrioadc lungi de tinp) esteacccacdrc
JJrl i l l ci dl ni nudrcr, h.rnr r(. .uhJoni ced . |L. r r I ( () r . , nr .
liorareatuncticidiastdicc r ventricululxi sle g.
Cardiomiopatiarestdctivd
Dcri prcvalenlacardioniopaticircstrictiveestefari. ea
esteinrpon:rntideoarcce evohrcazlcu fcnomene de insnfi-
fi&2./.9.cM H( ) seclilfc lticlla 5 cdncrc.DelirliL.rex
g dlcnlului
sist)llchcdlcadcicsiEaVS.InmgnBin irhsrn"afin\uhridc!-cclie cicnr:rL:rJ ,hj corgesli\;rclr\tJ l.,LrIr:,r:.,eIIii..,narer.
l;ri Jri,l, gi. l)e.,,enrc(d. .:rJ lrcL,.rri J,,rJir/iJ c.rpe-
nca itr constrictiva. exarncnul ccocardiograllc contribxind
subsl{ntialla diferenlierca accs(ordounentirdfr.luc cvo-
lucazi.r,nbele cn disfunclicdirsl(ticna venlficLrluhri sreng
ti drcptiicu semne deinsulicicnlh crrdiacidfeflpli1101.
Asplctulecografic dccardi(nniopntic rcstfictivipoalcdcnv.r
tutildincrc$crcarigjditiliiplyctilor!cntdcul i(fibfozi).ciLii
dininfiltrarcaacesrora (lbstac&rdionrioprtie infiltfati!i) ll 11.
PrincipahI eleflicoldcliniloriuccoc.r|d iogrnficdcrivndin
dislirncliadiasroliciprimari rcrlizrta$i seevaftrcazi optim
nrirrccocardiogralic DopplcrinnxxlLrlI)( sau.lndcoscbi. DP
I)isfnncliadiisl(ticiicncnrt|i rrrdcriprclaxarc 0llcrfi iiinMi
Uccvcnl dc lip rcslricliv.rc\crl (\,czipcriirrlnrnlVS)
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