EPIDEMIOLOGY
PATHOPHYSIOLOGY
It is where ganglionic cells of
the myenteric and
submucosal plexuses in the
bowel aren't present
proximally from the anus to a
variable length along the
large intestine.
ASSESSMENT
History. Carefully gather a history from
the family caregivers, noting especially
the history of stooling, onset
constipation, character and odor of
stools, frequency of bowel movements,
and the presence of poor feeding habits,
anorexia, and irritability.
Physical examination. During the
physical exam, observe for distended
abdomen and signs of poor nutrition;
record weight and vital signs.
MANAGEMENT
Initial therapy
Decompression
Diet
Antibiotics
TRANSMISSION
It occurs in approximately 1 per
If a family has a child with
5000 live births. The worldwide
Hirschsprung's disease, there is
prevalence may vary by region
a 3 to 12 percent chance that
and has been shown to be as
another baby from the same
high as 1 per 3000 live births in
parents will also have the
the Federated States of
disease. Children with Down
Micronesia.
syndrome have a higher risk as
well.
DIAGNOSIS
Hirschsprung
Constipation
Imbalanced nutrition
Fear
Disease
Risk for impaired skin integrity .
Acute Pain
Deficient fluid volume
Impaired oral and nasal mucous
membranes
SIGNS &
SYMPTOMS INTERVENTION
failure to have a bowel
movement in the first 48 hours Promote skin integrity
of life. Promote comfort
abdominal distention Maintain fluid balance
gradual onset of vomiting. Provide oral and nasal care
fever. Provide family teaching
constipation or failure to pass
regular bowel movements.