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Aorta
Aorta
zz
Anatomie
Diagram of the aortic root as seen at echocardiography. The aortic diameter should be measured at the aortic annulus (1), the sinuses of Valsalva (2), the supra-aortic ridge (3), and the proximal ascending aorta (4). In Marfan syndrome, dilatation usually starts at the sinuses of Valsalva, so this measurement is critical in monitoring the early evolution of the condition. Diameters must be related to normal values for age and body surface area.
Aorta dimensies-TEE
Cohen et al made various cardiac measurements using transoesophageal echocardiography in a group of 60 normal adults. These authors found the following aortic dimensions:
Aortic Annulus Tran-sinus Sino-tubular junction Ascending aorta Aortic arch Area
1.4 - 2.6 cms 2.1 - 3.5 cms 1.7 - 3.4 cms 2.1 - 3.4 cms 2.0 - 3.6 cms 2.4 - 3.5 cms^2
Aorta dimensies-Ctscan
Hager et al who have reported the diameter of the thoracic aorta at various sites as measured by helical computed tomography. In a group of 70 normal adults, these authors reported the following aortic dimensions: Tran-sinus Ascending aorta Distal Aortic arch Diaphragm 2.98 +/- 0.46 cms 3.09 +/- 0.41 cms 2.47 +/- 0.40 cms 2.43 +/- 0.35 cms
* Variable autosomal dominant disorder, characteristically with cardiovascular, eye and skeletal, features. * The minimal birth incidence is 1 in 9800 * 27% of cases arise from new mutation * Mutation in fibrillin-1 on chromosome 15 is detected in 6691% of cases * Some cases may be due to mutation in TGFbetaRl or TGFbetaR2 * TGFbetaR1 or TGFbetaR2 are also associated with Loeys-Dietz syndrome, and TGFbetaR2 with familial thoracic aortic aneurysm * The clinical diagnosis in adults should be made using the Ghent criteria * The Ghent criteria are unreliable in children * Prophylactic medical treatment to protect the aorta with regular follow-up helps prevent or delay serious complications * Prophylactic aortic surgery should be considered when the aortic root at the Sinus of Valsalva exceeds 5 cm
Marfaan syndrome
Table 1. Ghent diagnostic nosology System Major criterion Involvement Skeletal At least 4 of the following features: 2 of the major features, or 1 major feature and 2 of the following: filled circle Pectus carinatum filled circle Pectus excavatum filled circle Pectus excavatum requiring surgery filled circle Joint hypermobility filled circle ULSR <0.86 or span:height >1.05 filled circle High palate with dental filled circle Wrist and thumb signs filled circle Crowding filled circle Scoliosis >20 or spondylolisthesis filled circle Characteristic face filled circle Reduced elbow extension (<170) filled circle Pes plenus filled circle Protrusio acetabulae Ocular Lens dislocation (ectopia lentis) Flat cornea Increased axial length of globe (causing myopia) Hypoplastic iris or ciliary muscle (causing decreased miosis) Cardiovascular Dilatation of the aortic root Mitral valve prolapse Dissection of the ascending aorta Dilatation of the pulmonary artery, below age 40 Calcified mitral annulus, below age 40 Other dilatation or dissection of the aorta Pulmonary None Spontaneous pneumothorax Apical blebs Skin/Integument None Striae atrophicae Recurrent or incisional hernia Dura Lumbosacral dural ectasia None Genetic findings Parent, child or sibling meets these criteria independently None Fibrillin 1 mutation known to cause Marfan syndrome Inheritance of DNA marker haplotype linked to Marfan syndrome in the family Abbreviations: ULSR, Upper:lower segment ratio. Having one of the features listed constitutes a major criterion or system involvement for all systems except the skeletal system, where more than one feature is needed. Next table | Figure and tables index
Aorta dissectie
Type B dissectie
Klassificatie
DEBAKEY: 1. Dissection involving the ascending and descending aorta and aortic arch (10 %). 2. Dissection involving only the ascending aorta and aortic arch (60%). 3. Dissection involving only the descending aorta only (30 % ). STANFORD: 'A'. Debakey types 1 and 2: i.e. involves the ascending aorta. 'B'. Debakey type 3: i.e. involves only the descending aorta. Although anatomically more specific than the Stanford classification, the Debakey system seems to be less-widely used and less clinically useful than the Stanford classification.
flow is occurring only in the true lumen and that spontaneous echo contrast is apparent in the false lumen. The true lumen also expands markedly during systole.
In this longitudinal view through the distal aortic arch, the flap of a Stanford type 'A' dissection is demonstrated
distal descending thoracic aorta, occlusion of the false lumen of a Stanford type 'A' dissection by fresh thrombus is demonstrated.
Aortic atheroma
distal aortic arch, a pedunculated plaque
the mid and distal ascending aorta and proximal arch are blind spots for TOE due to the interposition of the trachea between the oesophagus and aorta. Although images are frequently seen of these regions, the image quality is often too poor for accurate diagnostic information and epiaortic ultrasonography is necessary for proper examination of this area.
Atheroma scoring
Various atheroma scoring systems have been suggested. A system recently used by Wilson et al is: 1. Normal 2. Intimal thickening (> 2 mm) 3. Atheroma < 4 mm +/- Ca++ 4. Atheroma >= 4 mm +/- Ca++, 5. Any size mobile or ulcerated lesion +/- Ca++. This is very similar to the grading system advocated by Montgomery et al which is also widely used: 1. normal 2. intimal thickening 3. atheroma < 5 mm 4. atheroma > or = 5 mm 5. mobile lesion