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Osler Weber Rendu Syndrome
Osler Weber Rendu Syndrome
Osler Weber Rendu Syndrome
Rendu Syndrome
(Hereditary Hemorrhagic
Telangiectasia)
Supervisor:
dr. Amran Simanjuntak, Sp
THT-KL (K)
Presentator:
Nining Satriani
Department of Otorhinolaryngology
Novel Ramadhani RSU Haji Medan
Siti Rodiana Hasibuan FK UISU
INTRODUCTION
Osler-Weber-Rendu Syndrome or Hereditary
Haemoragic Telangiectasia (HHT) is an autosomal
dominant genetic disorder that leads to vascular
malformations in mucocutaneus tissues, visceral
organs, and the central nervous system.
Tahun Tahun Tahun
1896 1901 1907
EPISTAXIS
Commonly used:
- KTP (532 nm)
- Yag (1060 nm)
- Argon (500 nm)
Using a
microbrider to
remove septal
mucosa with
telangiectasia
Fenestrated split-
thickness skin graft